The International Classification of Headache Disorders, 3rd edition (beta version)


ICHD-3 code Diagnosis
1=migraine

1.1 Migraine without aura
1.2 Migraine with aura
1.2.1 Migraine with typical aura
1.2.1.1 Typical aura with headache
1.2.1.2 Typical aura without headache
1.2.2 Migraine with brainstem aura
1.2.3 Hemiplegic migraine
1.2.3.1 Familial hemiplegic migraine (FHM)
1.2.3.1.1 Familial hemiplegic migraine type 1 (FHM1)
1.2.3.1.2 Familial hemiplegic migraine type 2 (FHM2)
1.2.3.1.3 Familial hemiplegic migraine type 3 (FHM3)
1.2.3.1.4 Familial hemiplegic migraine, other loci
1.2.3.2 Sporadic hemiplegic migraine
1.2.4 Retinal migraine
1.3 Chronic migraine
1.4 Complications of migraine
1.4.1 Status migrainosus
1.4.2 Persistent aura without infarction
1.4.3 Migrainous infarction
1.4.4 Migraine aura-triggered seizure
1.5 Probable migraine
1.5.1 Probable migraine without aura
1.5.2 Probable migraine with aura
1.6 Episodic syndromes that may be associated with migraine
1.6.1 Recurrent gastrointestinal disturbance
1.6.1.1 Cyclical vomiting syndrome
1.6.1.2 Abdominal migraine
1.6.2 Benign paroxysmal vertigo
1.6.3 Benign paroxysmal torticollis

2=Tension-type headache (TTH)

2.1 Infrequent episodic tension-type headache
2.1.1 Infrequent episodic tension-type headache associated with pericranial tenderness
2.1.2 Infrequent episodic tension-type headache not associated with pericranial tenderness
2.2 Frequent episodic tension-type headache
2.2.1 Frequent episodic tension-type headache associated with pericranial tenderness
2.2.2 Frequent episodic tension-type headache not associated with pericranial tenderness
2.3 Chronic tension-type headache
2.3.1 Chronic tension-type headache associated with pericranial tenderness
2.3.2 Chronic tension-type headache not associated with pericranial tenderness
2.4 Probable tension-type headache
2.4.1 Probable infrequent episodic tension-type headache
2.4.2 Probable frequent episodic tension-type headache
2.4.3 Probable chronic tension-type headache

3. Trigeminal autonomic cephalalgias (TACs)

3.1 Cluster headache
3.1.1 Episodic cluster headache
3.1.2 Chronic cluster headache
3.2 Paroxysmal hemicrania
3.2.1 Episodic paroxysmal hemicrania
3.2.2 Chronic paroxysmal hemicrania
3.3 Short-lasting unilateral neuralgiform headache attacks
3.3.1 Short-lasting unilateral neuralgiform headache attacks with conjunctival injection and
tearing (SUNCT)
3.3.1.1 Episodic SUNCT
3.3.1.2 Chronic SUNCT
3.3.2 Short-lasting unilateral neuralgiform headache attacks with cranial autonomic
symptoms (SUNA)
3.3.2.1 Episodic SUNA
3.3.2.2 Chronic SUNA
3.4 Hemicrania continua
3.5 Probable trigeminal autonomic cephalalgia
3.5.1 Probable cluster headache
3.5.2 Probable paroxysmal hemicrania
3.5.3 Probable short-lasting unilateral neuralgiform headache attacks
3.5.4 Probable hemicrania continua

4. Other primary headache disorders

4.1 Primary cough headache
4.1.1 Probable primary cough headache
4.2 Primary exercise headache
4.2.1 Probable primary exercise headache
4.3 Primary headache associated with sexual activity
4.3.1 Probable primary headache associated with sexual activity
4.4 Primary thunderclap headache
4.5 Cold-stimulus headache
4.5.1 Headache attributed to external application of a cold stimulus
4.5.2 Headache attributed to ingestion or inhalation of a cold stimulus
4.5.3 Probable cold-stimulus headache
4.5.3.1 Headache probably attributed to external application of a cold stimulus
4.5.3.2 Headache probably attributed to ingestion or inhalation of a cold stimulus
4.6 External-pressure headache
4.6.1 External-compression headache
4.6.2 External-traction headache
4.6.3 Probable external-pressure headache
4.6.3.1 Probable external-compression headache
4.6.3.2 Probable external-traction headache
4.7 Primary stabbing headache
4.7.1 Probable primary stabbing headache
4.8 Nummular headache
4.8.1 Probable nummular headache
4.9 Hypnic headache
4.9.1 Probable hypnic headache
4.10 New daily persistent headache (NDPH)
4.10.1 Probable new daily persistent headache

5. Headache attributed to trauma or injury to the head and/or neck

5.1 Acute headache attributed to traumatic injury to the head
5.1.1 Acute headache attributed to moderate or severe traumatic injury to the head
5.1.2 Acute headache attributed to mild traumatic injury to the head
5.2 Persistent headache attributed to traumatic injury to the head
5.2.1 Persistent headache attributed to moderate or severe traumatic injury to the head
5.2.2 Persistent headache attributed to mild traumatic injury to the head
5.3 Acute headache attributed to whiplash
5.4 Persistent headache attributed to whiplash
5.5 Acute headache attributed to craniotomy
5.6 Persistent headache attributed to craniotomy

6. Headache attributed to cranial or cervical vascular disorder

6.1 Headache attributed to ischaemic stroke or transient ischaemic attack
6.1.1 Headache attributed to ischaemic stroke (cerebral infarction)
6.1.2 Headache attributed to transient ischaemic attack (TIA)
6.2 Headache attributed to non-traumatic intracranial haemorrhage
6.2.1 Headache attributed to non-traumatic intracerebral haemorrhage
6.2.2 Headache attributed to non-traumatic subarachnoid haemorrhage (SAH)
6.2.3 Headache attributed to non-traumatic acute subdural haemorrhage (ASDH)
6.3 Headache attributed to unruptured vascular malformation
6.3.1 Headache attributed to unruptured saccular aneurysm
6.3.2 Headache attributed to arteriovenous malformation (AVM)
6.3.3 Headache attributed to dural arteriovenous fistula (DAVF)
6.3.4 Headache attributed to cavernous angioma
6.3.5 Headache attributed to encephalotrigeminal or leptomeningeal angiomatosis
(Sturge Weber syndrome) 6.4 Headache attributed to arteritis
6.4.1 Headache attributed to giant cell arteritis (GCA)
6.4.2 Headache attributed to primary angiitis of the central nervous system (PACNS)
6.4.3 Headache attributed to secondary angiitis of the central nervous system (SACNS)
6.5 Headache attributed to cervical carotid or vertebral artery disorder
6.5.1 Headache or facial or neck pain attributed to cervical carotid or vertebral artery
dissection
6.5.2 Post-endarterectomy headache
6.5.3 Headache attributed to carotid or vertebral angioplasty
6.6 Headache attributed to cerebral venous thrombosis (CVT)
6.7 Headache attributed to other acute intracranial arterial disorder
6.7.1 Headache attributed to an intracranial endovascular procedure
6.7.2 Angiography headache
6.7.3 Headache attributed to reversible cerebral vasoconstriction syndrome (RCVS)
6.7.3.1 Headache probably attributed to reversible cerebral vasoconstriction
syndrome (RCVS)
6.7.4 Headache attributed to intracranial arterial dissection
6.8 Headache attributed to genetic vasculopathy
6.8.1 Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and
Leukoencephalopathy (CADASIL)
6.8.2 Mitochondrial Encephalopathy, Lactic Acidosis and Stroke-like episodes (MELAS)
6.8.3 Headache attributed to another genetic vasculopathy
6.9 Headache attributed to pituitary apoplexy

7. Headache attributed to non-vascular intracranial disorder

7.1 Headache attributed to increased cerebrospinal fluid pressure
7.1.1 Headache attributed to idiopathic intracranial hypertension (IIH)
7.1.2 Headache attributed to intracranial hypertension secondary to metabolic, toxic or
hormonal causes
7.1.3 Headache attributed to intracranial hypertension secondary to hydrocephalus
7.2 Headache attributed to low cerebrospinal fluid pressure
7.2.1 Post-dural puncture headache
7.2.2 CSF fistula headache
7.2.3 Headache attributed to spontaneous intracranial hypotension
7.3 Headache attributed to non-infectious inflammatory disease
7.3.1 Headache attributed to neurosarcoidosis
7.3.2 Headache attributed to aseptic (non-infectious) meningitis
7.3.3 Headache attributed to other non-infectious inflammatory disease
7.3.4 Headache attributed to lymphocytic hypophysitis
7.3.5 Syndrome of transient Headache and Neurological Deficits with cerebrospinal fluid
Lymphocytosis (HaNDL)
7.4 Headache attributed to intracranial neoplasia
7.4.1 Headache attributed to intracranial neoplasm
7.4.1.1 Headache attributed to colloid cyst of the third ventricle
7.4.2 Headache attributed to carcinomatous meningitis
7.4.3 Headache attributed to hypothalamic or pituitary hyper- or hyposecretion
7.5 Headache attributed to intrathecal injection
7.6 Headache attributed to epileptic seizure
7.6.1 Hemicrania epileptica
7.6.2 Post-ictal headache
7.7 Headache attributed to Chiari malformation type I (CM1)
7.8 Headache attributed to other non-vascular intracranial disorder

8. Headache attributed to a substance or its withdrawal

8.1 Headache attributed to use of or exposure to a substance
8.1.1 Nitric oxide (NO) donor-induced headache
8.1.1.1 Immediate NO donor-induced headache
8.1.1.2 Delayed NO donor-induced headache
8.1.2 Phosphodiesterase (PDE) inhibitor-induced headache
8.1.3 Carbon monoxide (CO)-induced headache
8.1.4 Alcohol-induced headache
8.1.4.1 Immediate alcohol-induced headache
8.1.4.2 Delayed alcohol-induced headache
8.1.5 Headache induced by food and/or additive
8.1.5.1 Monosodium glutamate (MSG)-induced headache
8.1.6 Cocaine-induced headache
8.1.7 Histamine-induced headache
8.1.7.1 Immediate histamine-induced headache
8.1.7.2 Delayed histamine-induced headache
8.1.8 Calcitonin gene-related peptide (CGRP)-induced headache
8.1.8.1 Immediate CGRP-induced headache
8.1.8.2 Delayed CGRP-induced headache
8.1.9 Headache attributed to exogenous acute pressor agent
8.1.10 Headache attributed to occasional use of non-headache medication
8.1.11 Headache attributed to long-term use of non-headache medication
8.1.12 Headache attributed to exogenous hormone
8.1.13 Headache attributed to use of or exposure to other substance
8.2 Medication-overuse headache (MOH)
8.2.1 Ergotamine-overuse headache
8.2.2 Triptan-overuse headache
8.2.3 Simple analgesic-overuse headache
8.2.3.1 Paracetamol (acetaminophen)-overuse headache
8.2.3.2 Acetylsalicylic acid-overuse headache
8.2.3.3 Other non-steroidal anti-inflammatory drug (NSAID)-overuse headache
8.2.4 Opioid-overuse headache
8.2.5 Combination-analgesic-overuse headache
8.2.6 Medication-overuse headache attributed to multiple drug classes not individually
overused
8.2.7 Medication-overuse headache attributed to unverified overuse of multiple drug classes
8.2.8 Medication-overuse headache attributed to other medication
8.3 Headache attributed to substance withdrawal
8.3.1 Caffeine-withdrawal headache
8.3.2 Opioid-withdrawal headache
8.3.3 Oestrogen-withdrawal headache
8.3.4 Headache attributed to withdrawal from chronic use of other substance

9. Headache attributed to infection

9.1 Headache attributed to intracranial infection
9.1.1 Headache attributed to bacterial meningitis or meningoencephalitis
9.1.1.1 Acute headache attributed to bacterial meningitis or meningoencephalitis
9.1.1.2 Chronic headache attributed to bacterial meningitis or meningoencephalitis
9.1.1.3 Persistent headache attributed to past bacterial meningitis or meningoencephalitis
9.1.2 Headache attributed to viral meningitis or encephalitis
9.1.2.1 Headache attributed to viral meningitis
9.1.2.2 Headache attributed to viral encephalitis
9.1.3 Headache attributed to intracranial fungal or other parasitic infection
9.1.3.1 Acute headache attributed to intracranial fungal or other parasitic infection
9.1.3.2 Chronic headache attributed to intracranial fungal or other parasitic infection
9.1.4 Headache attributed to brain abscess
9.1.5 Headache attributed to subdural empyema
9.2 Headache attributed to systemic infection
9.2.1 Headache attributed to systemic bacterial infection
9.2.1.1 Acute headache attributed to systemic bacterial infection
9.2.1.2 Chronic headache attributed to systemic bacterial infection
9.2.2 Headache attributed to systemic viral infection
9.2.2.1 Acute headache attributed to systemic viral infection
9.2.2.2 Chronic headache attributed to systemic viral infection
9.2.3 Headache attributed to other systemic infection
9.2.3.1 Acute headache attributed to other systemic infection
9.2.3.2 Chronic headache attributed to other systemic infection

10. Headache attributed to disorder of homoeostasis

10.1 Headache attributed to hypoxia and/or hypercapnia
10.1.1 High-altitude headache
10.1.2 Headache attributed to aeroplane travel
10.1.3 Diving headache
10.1.4 Sleep apnoea headache
10.2 Dialysis headache
10.3 Headache attributed to arterial hypertension
10.3.1 Headache attributed to phaeochromocytoma
10.3.2 Headache attributed to hypertensive crisis without hypertensive encephalopathy
10.3.3 Headache attributed to hypertensive encephalopathy
10.3.4 Headache attributed to pre-eclampsia or eclampsia
10.3.5 Headache attributed to autonomic dysreflexia
10.4 Headache attributed to hypothyroidism
10.5 Headache attributed to fasting
10.6 Cardiac cephalalgia
10.7 Headache attributed to other disorder of homoeostasis

11. Headache or facial pain attributed to disorder of the cranium, neck, eyes, ears, nose, sinuses,
teeth, mouth or other facial or cervical structure

11.1 Headache attributed to disorder of cranial bone
11.2 Headache attributed to disorder of the neck
11.2.1 Cervicogenic headache
11.2.2 Headache attributed to retropharyngeal tendonitis
11.2.3 Headache attributed to craniocervical dystonia
11.3 Headache attributed to disorder of the eyes
11.3.1 Headache attributed to acute glaucoma
11.3.2 Headache attributed to refractive error
11.3.3 Headache attributed to heterophoria or heterotropia (latent or persistent squint)
11.3.4 Headache attributed to ocular inflammatory disorder
11.3.5 Headache attributed to trochleitis
11.4 Headache attributed to disorder of the ears
11.5 Headache attributed to disorder of the nose or paranasal sinuses
11.5.1 Headache attributed to acute rhinosinusitis
11.5.2 Headache attributed to chronic or recurring rhinosinusitis
11.6 Headache attributed to disorder of the teeth or jaw
11.7 Headache attributed to temporomandibular disorder (TMD)
11.8 Head or facial pain attributed to inflammation of the stylohyoid ligament
11.9 Headache or facial pain attributed to other disorder of cranium, neck, eyes, ears, nose,
sinuses, teeth, mouth or other facial or cervical structure

12. Headache attributed to psychiatric disorder

12.1 Headache attributed to somatization disorder
12.2 Headache attributed to psychotic disorder

13. Painful cranial neuropathies and other facial pains

13.1 Trigeminal neuralgia
13.1.1 Classical trigeminal neuralgia
13.1.1.1 Classical trigeminal neuralgia, purely paroxysmal
13.1.1.2 Classical trigeminal neuralgia with concomitant persistent facial pain
13.1.2 Painful trigeminal neuropathy
13.1.2.1 Painful trigeminal neuropathy attributed to acute Herpes zoster
13.1.2.2 Post-herpetic trigeminal neuropathy
13.1.2.3 Painful post-traumatic trigeminal neuropathy
13.1.2.4 Painful trigeminal neuropathy attributed to multiple sclerosis (MS) plaque
13.1.2.5 Painful trigeminal neuropathy attributed to space-occupying lesion
13.1.2.6 Painful trigeminal neuropathy attributed to other disorder
13.2 Glossopharyngeal neuralgia
13.3 Nervus intermedius (facial nerve) neuralgia
13.3.1 Classical nervus intermedius neuralgia
13.3.2 Nervus intermedius neuropathy attributed to Herpes zoster
13.4 Occipital neuralgia
13.5 Optic neuritis
13.6 Headache attributed to ischaemic ocular motor nerve palsy
13.7 Tolosa-Hunt syndrome
13.8 Paratrigeminal oculosympathetic (Raeder’s) syndrome
13.9 Recurrent painful ophthalmoplegic neuropathy
13.10 Burning mouth syndrome (BMS)
13.11 Persistent idiopathic facial pain (PIFP)
13.12 Central neuropathic pain
13.12.1 Central neuropathic pain attributed to multiple sclerosis (MS)
13.12.2 Central post-stroke pain (CPSP)

14. Other headache disorders

14.1 Headache not elsewhere classified
14.2 Headache unspecified